- 1 in 30,000 births.
- More common in males than in females: 2 to 1.
- Abdominal wall mass in the suprapubic region below a low insertion of the umbilical cord.
- Non-visible bladder with normal volume of amniotic fluid.
- Widely separated pubic bones, short and broad penis in males, hemiclitoris on either side of the bladder in females.
The incidence of chromosomal abnormalities and genetic syndromes is not increased.
- Detailed ultrasound examination.
- Invasive testing to determine the genetic sex of the fetus.
- Follow-up should be standard.
- Place: hospital with neonatal intensive care and pediatric surgery.
- Time: 38 weeks.
- Method: induction of labor aiming for vaginal delivery.
- Survival rate is >95%. Surgery aims to achieve bladder closure and urinary continence, and epispadias repair.
- No increased risk of recurrence.