- 1 in 100,000 births.
- Enlarged hyperechogenic lung with dilated bronchial tree resulting in mediastinal shift to the contralateral side.
- Presence of ascites (resulting from central venous compression) is a bad prognostic factor.
- The incidence of chromosomal abnormalities and genetic syndromes is not increased.
- Detailed ultrasound examination.
- Ultrasound scans every 4 weeks to monitor the evolution of the condition.
- Place: hospital with neonatal intensive care and pediatric surgery.
- Time: 38 weeks.
- Method: cesarean section because of need for immediate postnatal resuscitation and intubation.
- High rate of perinatal mortality.
- No increased risk of recurrence.