Prevalence:

• 1 in 100,000 births.

Ultrasound diagnosis:

• Enlarged hyperechogenic lung with dilated bronchial tree resulting in mediastinal shift to the contralateral side.
• Presence of ascites (resulting from central venous compression) is a bad prognostic factor.

Associated abnormalities:

• The incidence of chromosomal abnormalities and genetic syndromes is not increased.

Investigations:

• Detailed ultrasound examination.

Follow up:

• Ultrasound scans every 4 weeks to monitor the evolution of the condition.

Delivery:

• Place: hospital with neonatal intensive care and pediatric surgery.
• Time: 38 weeks.
• Method: cesarean section because of need for immediate postnatal resuscitation and intubation.

Prognosis:

• High rate of perinatal mortality.

Recurrence:

• No increased risk of recurrence.